Dropped head and man-in-barrel syndrome in amyotrophic lateral sclerosis
نویسندگان
چکیده
We report a case of progressive symmetric brachial weakness followed by cervical muscle weakness. The electromyogram confirmed the diagnosis of amyotrophic lateral sclerosis. After 3 years the patient remained able to walk unassisted and without significant bulbar manifestations or upper neuron signs. The concomitant presence of dropped head syndrome and man-in-barrel syndrome in an amyotrophic lateral sclerosis patient makes our case unique.
منابع مشابه
Man-in-the-barrel syndrome as an atypical form of Amyotrophic Lateral Sclerosis
Rev Neurocienc 2008:in press Recebido em: 21/11/07 Revisado em: 22/11/07 a 04/05/08 Aceito em: 05/05/08 Conflito de interesses: não Endereço para correspondência: Marco Orsini Rua Prof. Miguel Couto 322/1001 24230-240 Niterói, RJ E-mail: [email protected] Research was made in Neuromuscular Disease Outpatient Division, Departament of Neurology at Federal Fluminense University, Niterói, RJ...
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OBJECTIVE To report on 9 patients presenting with sporadic motor neuron disease , who over a long period of time evolved with a symmetrical proximal brachial amyotrophic diplegia. METHODS Nine patients were followed-up who , displayed, since onset, a progressive limitation of arm flexion/abduction resulting in a peculiar posture with both hands hanging loosely beside the trunk. Electrophysiol...
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عنوان ژورنال:
دوره 2017 شماره
صفحات -
تاریخ انتشار 2017